Volume 2, Issue 3, September 2018, Page: 65-67
Ebstein Anomaly in a 60 Years Patient: A Lucky Finding
Randa Tabbah, Department of Cardiology, Holy Spirit University, Kaslik, Lebanon
Raffy Karaminissian, Department of Cardiology, Lebanese American University, Jbeil, Lebanon
Received: Sep. 13, 2018;       Accepted: Sep. 27, 2018;       Published: Oct. 30, 2018
DOI: 10.11648/j.ccr.20180203.14      View  371      Downloads  28
Ebstein anomaly is a rare congenital disease of the tricuspid valve (<1%) diagnosed at all ages. A single case of an 85 y old patient was reported in 1979 as the longest survival with ebstein anomaly who had no cardiac symptoms until 79 years old. The aim of this case report is to highlight the need for an early echocardiographic diagnosis of this disease to prevent sudden death from arrhythmias or other complications because as we see patients with ebstein anomaly can live a healthy long life asymptomatic. The patient described in this case is a 60 years old male diabetic and heavy smoker, who presented to the cardiology department with fatigue and atypical angina with dyspnea on moderate effort. Cardiac ultrasound was in favor of an isolated Ebstein anomaly type A, with partial atrialization of the right ventricle (RV) with an adequate volume of the right ventricle (17cm2) and no specific other associated anomalies. Symptoms described by the patient were purely pulmonary due to a mild obstructive disease. Patient was diagnosed with chronic obstructive lung disease due to his smoking habits. Reaching this age and being asymptomatic with conserved RV and LV function is a sign of good outcome. This case was an interesting lucky finding. It was astonishing to see a patient surviving this anomaly at 60 years old asymptomatically.
Ebstein Anomaly, Asymptomatic, Atrialization
To cite this article
Randa Tabbah, Raffy Karaminissian, Ebstein Anomaly in a 60 Years Patient: A Lucky Finding, Cardiology and Cardiovascular Research. Vol. 2, No. 3, 2018, pp. 65-67. doi: 10.11648/j.ccr.20180203.14
Copyright © 2018 Authors retain the copyright of this article.
This article is an open access article distributed under the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0/) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
Oxenius A, Attenhofer Jost CH, Prêtre R et al, Management and outcome of Ebstein's anomaly in children. Cardiol Young. 2013 Feb; 23(1):27-34.
Boyle B, Garne E, Loane M et al, The changing epidemiology of Ebstein's anomaly and its relationship with maternal mental healthconditions: a European registry-based study. Cardiol Young. 2017 May; 27 (4):677-685.
Luu Q, Choudhary P, Jackson D et al, Ebstein's anomaly in those surviving to adult life - a single centre experience. Heart Lung Circ. 2015 Oct; 24(10):996-1001.
Seward JB, Tajik AJ, Feist DJ et al, Ebstein's anomaly in an 85-year-old man. Mayo ClinProc. 1979 Mar; 54(3):193-6.
Shivapour JK, Sherwin ED, Alexander MEet al. Utility of preoperative electrophysiologic studies in patients with Ebstein's anomaly undergoing the Cone procedure. Heart Rhythm. 2014 Feb; 11(2):182-6.
Sherwin ED, Abrams DJ. Ebstein Anomaly. Card Electrophysiol Clin. 2017 Jun; 9(2):245-254.
Deal BJ, Mavroudis C. Arrhythmia Surgery for Adults with Congenital Heart Disease. Card Electrophysiol Clin. 2017 Jun; 9(2):329-340.
Warnes CA, Williams RG, Bashore TM et al, ACC/AHA 2008 Guidelines for the Management of Adults with Congenital Heart Disease: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (writing committee to develop guidelines on the management of adults with congenital heart disease). Circulation. 2008 Dec 2; 118(23):e714-833.
Ciepłucha A, Trojnarska O, Kociemba A et al. Clinical aspects of myocardial fibrosis in adults with Ebstein's anomaly. Heart Vessels. 2018 Sep; 33(9):1076-1085.
Celermajer DS1, Bull C, Till JA et al. Ebstein's anomaly: presentation and outcome from fetus to adult. J Am Coll Cardiol. 1994 Jan; 23(1):170-6.
De Lemos JA, Delacretaz E, Piana RN et al. Images in cardiovascular medicine. Ebstein's anomaly associated with an anomalous coronaryartery, 2 myocardial bridges, and a mahaim fiber. Circulation. 1999 Oct 19; 100(16):1757-9.
Qureshi MY, O'Leary PW, Connolly HM. Cardiac imaging in Ebstein anomaly. Trends Cardiovasc Med. 2018 Aug; 28(6):403-409.
Greutmann M, Buechel ERV, Jost CA. Editorial commentary: The caveats of cardiac imaging in Ebstein anomaly. Trends Cardiovasc Med. 2018 Aug; 28(6):410-411.
Fratz S, Janello C, Müller D et al. The functional right ventricle and tricuspid regurgitation in Ebstein's anomaly. Int J Cardiol. 2013 Jul 15; 167(1):258-61.
Sherwin ED, Walsh EP, Abrams DJ. Variable QRS morphologies in Ebstein's anomaly: what is the mechanism? Heart Rhythm. 2013 Jun; 10(6):933-7.
Browse journals by subject