Volume 2, Issue 3, September 2018, Page: 65-67
Ebstein Anomaly in a 60 Years Patient: A Lucky Finding
Randa Tabbah, Department of Cardiology, Holy Spirit University, Kaslik, Lebanon
Raffy Karaminissian, Department of Cardiology, Lebanese American University, Jbeil, Lebanon
Received: Sep. 13, 2018;       Accepted: Sep. 27, 2018;       Published: Oct. 30, 2018
DOI: 10.11648/j.ccr.20180203.14      View  125      Downloads  5
Abstract
Ebstein anomaly is a rare congenital disease of the tricuspid valve (<1%) diagnosed at all ages. A single case of an 85 y old patient was reported in 1979 as the longest survival with ebstein anomaly who had no cardiac symptoms until 79 years old. The aim of this case report is to highlight the need for an early echocardiographic diagnosis of this disease to prevent sudden death from arrhythmias or other complications because as we see patients with ebstein anomaly can live a healthy long life asymptomatic. The patient described in this case is a 60 years old male diabetic and heavy smoker, who presented to the cardiology department with fatigue and atypical angina with dyspnea on moderate effort. Cardiac ultrasound was in favor of an isolated Ebstein anomaly type A, with partial atrialization of the right ventricle (RV) with an adequate volume of the right ventricle (17cm2) and no specific other associated anomalies. Symptoms described by the patient were purely pulmonary due to a mild obstructive disease. Patient was diagnosed with chronic obstructive lung disease due to his smoking habits. Reaching this age and being asymptomatic with conserved RV and LV function is a sign of good outcome. This case was an interesting lucky finding. It was astonishing to see a patient surviving this anomaly at 60 years old asymptomatically.
Keywords
Ebstein Anomaly, Asymptomatic, Atrialization
To cite this article
Randa Tabbah, Raffy Karaminissian, Ebstein Anomaly in a 60 Years Patient: A Lucky Finding, Cardiology and Cardiovascular Research. Vol. 2, No. 3, 2018, pp. 65-67. doi: 10.11648/j.ccr.20180203.14
Copyright
Copyright © 2018 Authors retain the copyright of this article.
This article is an open access article distributed under the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0/) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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